Anaesthetic Considerations in an Infant with Cryptophthalmos – Anophthalmos

Authors

  • Veena Asthana Department of Anaesthesiology, HIMS, SRHU, Baksar Wala, India
  • Vinayak Saran Department of Anaesthesiology, HIMS, SRHU, Baksar Wala, India
  • Amit Kumar Chauhan Department of Anaesthesiology, HIMS, SRHU, Baksar Wala, India
  • Sukhdeep Bains Department of Ophthalmology, HIMS, SRHU, Baksar Wala, India

Keywords:

Anaesthetic, Considerations, Infant, Cryptophthalmos, Anophthalmos, Syndrome

Abstract

Several instances of Cryptophthalmos-Anophthalmos syndrome, including Fraser’s syndrome have been documented and the various anomalies found associated have been known, including the anaesthetic complications in cardiac as well as other major surgeries. Here we discuss the anaesthetic management and considerations in a non-cardiac case, including the difficult airway, for which retro-molar technique of intubation was successfully performed after one unsuccessful direct laryngoscopy intubation attempt.

References

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Narang, M., Kumar, M. & Shah, D. Frasercryptophthalmos syndrome with colonic atresia. Indian J Pediatr 75, 189–191 (2008). https://doi.org/10.1007/s12098-008-0030-9

Shafeghati Y, Kniepert A, Vakili G, Zenker M. 2008. Fraser syndrome due to homozygosity for a splice site mutation of FREM2. Am J Med

Gent Part A 146A:529-531. https://doi.org/10.1002/ajmg.a.32091

Kalpana Kumari M K, Kamath S, Mysorekar VV, Nandini G. Fraser syndrome. Indian J Pathol Microbiol 2008;51:228-9. https://doi.org/10.4103/0377-4929.41664

Published

2023-04-30

Issue

Vol. 11

Section

Articles

License

Creative Commons License

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