Unusual, Rare Case of Ascending Aortic Atresia and Right Ventricle Dependent Coronary Circulation in a Newborn - Pages 1-5

Christopher F. Tirotta and E. Oliver Aregullin

The Heart Program of Miami Children’s Hospital, USA

DOI: http://dx.doi.org/10.14205/2310-9394.2014.02.01.1


We describe a newborn with complex, congenital cardiac anomalies, most notably single ventricle physiology, interruption/atresia of the ascending aorta and a coronary circulation that was totally Right Ventricle (RV) dependent. This arrangement left the coronary supply in a very precarious situation, theoretically much worse than most patients with Pulmonary Atresia/Intact Ventricular Septum (PA/IVS), since the entire coronary circulation was RV dependent. The patient underwent a palliative surgical correction, but expired the following day. We believe this is the first reported case in the literature with this constellation of lesions.

Keywords: RV Dependent, Pulmonary Atresia/Intact Ventricular Septum, Complete Atrioventricular Canal.